Transcatheter Sinus Venosus ASD Closure: A Case Series of First Ever Transcatheter Closure of the Defect in Pakistan
Authors
- Muhammad babar AFIC/NIHD, Rawalpindi, Pakistan
- Saima Rafique Department of Pediatirc Cardiology, Armed Forces Institute of Cardiology. Rawalpindi, Pakistan
- Khurram Akhtar Department of Pediatirc Cardiology, Armed Forces Institute of Cardiology. Rawalpindi, Pakistan
- Abubakar Sadiq Department of Pediatirc Cardiology, Armed Forces Institute of Cardiology. Rawalpindi, Pakistan
- Azizullah Azizullah Department of Pediatirc Cardiology, Armed Forces Institute of Cardiology. Rawalpindi, Pakistan
- Amjad Mehmood Department of Pediatirc Cardiology, Armed Forces Institute of Cardiology. Rawalpindi, Pakistan
- Maimoona Saeed Department of Pediatirc Cardiology, Armed Forces Institute of Cardiology. Rawalpindi, Pakistan
Keywords:
- Anomalous venous drainage,
- Interventionalists,
- Transcatheter,
- Sinus venosus
Abstract
Superior sinus venosus atrial septal defect is a direct communication between the right and left atrium located above the fossa ovalis below the junction of the superior vena cava and the right atrium. It is associated with partial anomalous pulmonary venous drainage, especially of the right upper and middle pulmonary veins. Over the years, surgical repair of the defect has been primary approach to close that defect. However, since 2014, percutaneous closure of the defect has gradually become a safe and effective alternative to surgery in carefully selected patients, although worldwide experience remains limited. This case series highlights three cases of first ever transcatheter sinus venosus atrial septal defect closures in Pakistan.
Understanding the anatomy of the crossroads formed by the Right Upper Pulmonary Vein (RUPV) ostium, the SVC orifice, the Right Atrium (RA), and the Left Atrium (LA) above the level of the unroofed atrial septum is key to appreciating the procedural concept. This article provides a comprehensive, up-to-date description of percutaneous management of SVD, detailing preprocedural screening, multimodality imaging for case planning and guidance, and procedural steps. It also summarizes a comprehensive overview of the contemporary clinical outcomes of the transcatheter SVD closure. It also underscores the importance of the fact that transcatheter closure of this defect can easily be achieved, significantly reducing patient’s morbidity as opposed to open heart surgery.
We believe that modified techniques along with growing experience of interventionalists all over the world will further enhance safety and expand the role of transcatheter closure of SVD.


